Solitary Fibrous Tumor of Orbit Mimicking Sarcoma in 14 Years Old Boy: A Rare Case Report

Abstract

A solitary fibrous tumor (SFT) is a rare spindle cell neoplasm representing <2% of all soft tissue tumors. SFT was first described in the pleura and previously thought to be arising from mesothelium but recent studies have shown that any part of the body can be affected. Here, we report a case of SFT arising from the extraconal compartment of the right eye of a 14-year-old boy who presented with painless, slowly progressive swelling of the right eye for two years. On the basis of clinical details, a diagnosis of sarcoma was made. MRI findings revealed a well-circumscribed heterogeneously enhancing extraconal right orbital lesion suggestive of low-grade sarcoma. The patient underwent wide local excision. Grossly, it was a grey-white firm tumor. Histopathological features and immunohistochemistry were consistent with solitary fibrous tumor.